Pleuropulmonary Blastoma in an Infant Presenting with Tension Pneumothorax
نویسنده
چکیده
Pleuropulmonary blastoma is one of the rarest tumours occurring in childhood. The pathogenesis and therapeutic management of this condition remain controversial. We report the case of an 8-month-old girl with cystic pleuropulmonary blastoma (type 1), presenting with respiratory distress and a tension pneumothorax. The clinical and radiological aspects of the pleuropulmonary blastoma are also discussed.
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